Primary Renal Leiomyosarcoma: Case Report and Review of the Literature

Renal leiomyosarcoma is an extremely rare malignant tumor. On clinical presentation and radio imaging it challenging to make accurate preoperative diagnosis. In our case, a 59-year-old female presented with history of left-sided flank pain, intermittent hematuria weight loss 6 months duration. She was known case hypertension diabetes mellitus 20 years on regular treatment. the abdomino-pelvis sonography showed exophytic cortical mass lesion measuring 4.0 x 3.8 cm lesion. Magnetic resonance abdomen pelvis (plain) shows well defined non encapsulated predominantly solid 4.3 4 4.5 noted in anterior cortex left kidney at interpolar region. There no evidence any regionalor distant metastesis. Patient underwent radical nephrectomy. histopathology reported as renal leiomyosarcoma. Immuhistochemistry smooth muscle actin diffusely desmin focally positive. We present this review primary for its presentation, radiographic findings, pathologic features.